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Keywords: Tuberous sclerosis
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Journal Articles
Subject Area:
Pharmacology , Pneumology
Journal: Respiration
Respiration (2017) 94 (6): 467–485.
Published Online: 23 November 2017
...Cécile Daccord; Laurent P. Nicod; Romain Lazor Cystic lung diseases constitute a distinct group of rare lung disorders, among which two result from monogenic defects affecting tumor suppressor genes: lymphangioleiomyomatosis, either sporadic or associated with tuberous sclerosis complex, and Birt...
Journal Articles
Subject Area:
Pharmacology , Pneumology
Journal: Respiration
Respiration (1990) 57 (6): 398–401.
Published Online: 20 January 2009
...Valeriano Foresti; Ornella Casati; Roberto Zubani; Antonio Villa We report on a male patient with tuberous sclerosis (adenoma sebaceum and digital fibromas, renal angiomyolipomas and subependymal brain calcifications), who presented with chylothorax. Chest CT scan did not show pulmonary parenchymal...
Journal Articles
Subject Area:
Pharmacology , Pneumology
Journal: Respiration
Respiration (1979) 37 (4): 238–240.
Published Online: 14 January 2009
.... Fibroleiomyomatous hamartoma Coin lesion Tuberous sclerosis Benign pulmonary lesions Respiration 37: 238-240 (1979) Fibroleiomyomatous Hamartoma of the Lung S. N. Hassani, R . Nuba and R . L. Bard State University o f New York, at Stony Brook; Radiology Department, Queens Hospital Center, Jam aica, N .Y...
Journal Articles
Subject Area:
Pharmacology , Pneumology
Journal: Respiration
Respiration (2002) 69 (3): 277–279.
Published Online: 19 June 2002
...Kazunori Fujitaka; Takeshi Isobe; Tetsuya Oguri; Masahiro Yamasaki; Mitsuru Miyazaki; Nobuoki Kohno; Yukio Takeshima; Kouki Inai We present a case of a 39-year-old woman with sporadic tuberous sclerosis (TSC), whose chest radiograph demonstrated bilateral diffuse nodular shadowing. A transbronchial...