...Léon Genecand; Julie Wacker; Ivan Guerreiro; Benoit Lechartier; Maurice Beghetti; Susanne Pohle; Andrei M. Darie; Mona Lichtblau; Silvia Ulrich; Sabina A. Guler; Frédéric Lador; On behalf of the Swiss Society of Pulmonary Hypertension Background: Pulmonary hypertension (PH) complicating...

...Mona Lichtblau; Frédéric Lador; Benoit Lechartier; Jana Maria Ellegast; Susanne Pohle; Helga Preiss; Leon Genecand; Carmen Wick; Silvia Ulrich; Lena Reimann Introduction: Hematological and oncological diseases collectively affect a substantial number of patients. Pulmonary hypertension (PH...

... vascular disease (PVD), defined as pulmonary arterial and distal chronic thromboembolic pulmonary hypertension (CTEPH), and may improve exercise performance. Methods: We investigated the effect of 5 weeks of AZA (250 mg bid) versus placebo on maximal load during incremental cycling ramp exercise...

... and extrinsic compression of adjacent bronchovascular structures. FM-associated pulmonary hypertension (FM-PH) is a serious complication of FM, resulting from the external compression of lung vessels. Pathologic assessment is important for etiologic diagnosis and effective treatment of this disease. Case...

...Elena Pfeuffer-Jovic; Franziska Joa; Michael Halank; Jens-Holger Krannich; Matthias Held Introduction: Anxiety and depression are common in pulmonary hypertension (PH) and health-related quality of life (HRQoL) is reduced. Sufficient analyses in incident and prevalent patients are lacking, so we...

...Léon Genecand; Dan Adler; Maurice Beghetti; Frédéric Lador Background: Cardiac output determination is essential in precapillary pulmonary hypertension. While direct Fick is the gold standard, thermodilution is commonly used as the reference method. Moving to noninvasive methods would be highly...

...Eglė Palevičiūtė; Lina Gumbienė; Elena Jurevičienė; Toma Šimbelytė; Ieva Laucevičienė; Aleksandras Laucevičius; Jūratė Barysienė; Christina A. Eichstaedt; Nicola Benjamin; Ekkehard Grünig; Jelena Čelutkienė Background: Pulmonary hypertension (PH) is a severe progressive disease, associated...

... and AMLs (1,179 pg/mL) ( p < 0.005). Cystic lung diseases Lymphangioleiomomatosis mTOR inhibitors Sirolimus Pulmonary hypertension Lymphangioleiomyomatosis (LAM) is a rare multisystem disease that predominantly affects women and is characterized by cystic lung destruction, renal...

... and interrelation of sleep-disordered breathing and nocturnal hypoxemia in patients with precapillary pulmonary hypertension (PH) is not fully understood. Methods: Seventy-one patients with PH (age 63 ± 15 years, 41% male) and 35 matched controls were enrolled. Patients with PH underwent clinical examination...

... with PAH and persistent/inoperable chronic thromboembolic pulmonary hypertension (CTEPH). Method: From the previous RCT, 43 out of 87 patients with severe PAH ( n = 29) and CTEPH ( n = 14) had complete haemodynamic examinations at baseline and after 15 weeks by right heart catheterization and were analysed...

...Michael Westhoff; Patric Litterst; Ralf Ewert Background: Combined pulmonary fibrosis and emphysema (CPFE) is a distinct entity among fibrosing lung diseases with a high risk for lung cancer and pulmonary hypertension (PH). Notably, concomitant PH was identified as a negative prognostic indicator...

...Marieke C. van der Molen; Jorine E. Hartman; Karin Klooster; Huib A.M. Kerstjens; Joost van Melle; Tineke P. Willems; Dirk-Jan Slebos Background: Currently, patients with COPD who are evaluated for bronchoscopic treatments are routinely screened for pulmonary hypertension (PH) and systolic left...

...Christian Nagel; Mohammed Nasereddin; Nicola Benjamin; Benjamin Egenlauf; Satenik Harutyunova; Christina A. Eichstaedt; Panagiota Xanthouli; Eckhard Mayer; Ekkehard Grünig; Stefan Guth Background: Data on exercise training in chronic thromboembolic pulmonary hypertension (CTEPH) after pulmonary...

... to persons or property resulting from any ideas, methods, instructions or products referred to in the content or advertisements. Altitude Chronic obstructive pulmonary disease Echocardiography Pulmonary hypertension Despite an increasing prevalence of chronic obstructive pulmonary disease...

...David K. Yoo; Maurizio Zompatori; Annapina Barrile; Giorgia Rossi; Dejanira D’Amato; Gianluigi Sergiacomi; Paola Rogliani; Marco Mura Background: Associated pulmonary hypertension (APH) is frequently observed in fibrosing interstitial pneumonias (FIP), such as idiopathic pulmonary fibrosis (IPF...

...David Montani; Julien Henry; Caroline O’Connell; Xavier Jaïs; Vincent Cottin; David Launay; Gilbert Habib; Arnaud Bourdin; Mitja Jevnikar; Laurent Savale; Laurence Rottat; Gérald Simonneau; Olivier Sitbon; Marc Humbert; Yannick Allanore Background: Precapillary pulmonary hypertension (PH...

...Marion Dupuis; Elise Noel-Savina; Gregoire Prévot; Laurent Tétu; Fabien Pillard; Daniel Rivière; Alain Didier Background: Cardiac output (CO) is a prognostic factor in pulmonary hypertension (PH). Right heart catheterisation using the direct Fick method or thermodilution (TD) is the reference...

..., quality or safety. The publisher and the editor(s) disclaim responsibility for any injury to persons or property resulting from any ideas, methods, instructions or products referred to in the content or advertisements. Pulmonary hypertension Heritable pulmonary arterial hypertension Hereditary...

... telangiectasia Pulmonary arteriovenous malformations Pulmonary hypertension Anemia Rare vascular disease Pathogenic ENG , ACVRL1 , and SMAD4 sequence variants can generate the full spectrum of vascular lesions in HHT, including pulmonary, cerebral, hepatic, and spinal involvement, though ENG...

...Robert Thurnheer; Silvia Ulrich; Konrad E. Bloch Among patients with sleep apnea the reported prevalence of precapillary pulmonary hypertension (PH) has varied largely, depending on patient selection, disease definition, and associated conditions, in particular chronic pulmonary disease. However...