1-4 of 4
Keywords: Primary adrenal insufficiency
Close
Follow your search
Access your saved searches in your account

Would you like to receive an alert when new items match your search?
Close Modal
Sort by
Journal Articles
Horm Res Paediatr (2018) 89 (5): 341–351.
Published Online: 06 June 2018
.... Adrenal insufficiency Congenital adrenal hyperplasia Adrenal crisis Hypopituitarism Primary adrenal insufficiency Secondary adrenal insufficiency Epidemiology Glucocorticoid National Institutes of Health (NIH) 10.13039/100000002 An adrenal crisis (AC) is an acute, life...
Journal Articles
Horm Res Paediatr (2018) 89 (3): 205–210.
Published Online: 22 March 2018
...Ahlee Kim; Masanobu Fujimoto; Vivian Hwa; Philippe Backeljauw; Andrew Dauber Background/Aims: Cholesterol side-chain cleavage enzyme (P450scc) deficiency is a rare genetic disorder causing primary adrenal insufficiency with or without a 46,XY disorder of sexual development (DSD). Herein, we report...
Journal Articles
Journal Articles
Horm Res Paediatr (2014) 82 (3): 145–157.
Published Online: 01 August 2014
...Jana Malikova; Christa E. Flück Primary adrenal insufficiency (PAI) is a rare condition in childhood which is either inherited (mostly) or acquired. It is characterized by glucocorticoid and maybe mineralocorticoid deficiency. The most common form in children is 21-hydroxylase deficiency, which...