...So Young Park; Min Jeong Wang; Jae-Won Jang; Young Ho Park; Jae-Sung Lim; Young Chul Youn; Jungeun Kim; SangYun Kim Background: Clinical diagnosis of sporadic Creutzfeldt-Jakob disease (sCJD) is currently based on changes occurring in the late disease stages, which limits early-stage detection...

...Hung-Ming Wu; Chin-Song Lu; Chin-Chang Huang; Rong-Kuo Lyu; Rou-Shayn Chen; Yih-Ru Wu; Yi-Chun Chen; Szu-Chia Lai; June Hung; Yu-Tai Tsai; Cheng-Hong Toh; Hung-Chou Kuo Objective: To ascertain the characteristics of patients with sporadic Creutzfeldt-Jakob disease (CJD) and to determine...

.... Asperger syndrome Creutzfeldt-Jakob disease Euthanasia Gerstmann-Sträussler-Scheinker disease Hallervorden-Spatz syndrome Lewy body dementia Niemann-Pick disease Rett syndrome Seitelberger disease Wallenberg’s syndrome The 1920s were a period of exceptional advancement...

..., instructions or products referred to in the content or advertisements. Alfons Maria Jakob Alpers disease Creutzfeldt-Jakob disease History of neuroscience History of neuropathology A notable representative of German neuropathology [ 1,2,3 ], Bavarian neurologist Alfons Maria Jakob (fig. 1...

...U.A. Aguglia; G. Farnarier; H. Regis; R.L. Oliveri; A.Q. Quattrone Eight patients presenting with intermediate or terminal evolution of Creutzfeldt-Jakob disease (CJD) were investigated by means of evoked potentials. Fifteen age-matched healthy subjects served as controls. The 8 patients had well...

...N. Heye; J. Cervós-Navarro Focal involvement can be assumed in the initial stage of Creutzfeldt-Jakob disease (CJD). We correlated the clinical, electroencephalographic and neuropathological findings in 13 cases of CJD with special reference to focal or lateralized changes. Eight cases showed...

...Ming-Shung Su; Shuu-Jiun Wang; Hung Chiang; Jyh-Seng Wang; Yuan-Ann Tan; Jong-Ling Fuh; Hsiu-Chih Liu We report a case of the unusual panencephalopathic type of Creutzfeldt-Jakob disease (CJD) in Taiwan. This 59-year-old woman presented in 1983 with typical clinical manifestations of CJD and died...

...Jan-Edvin Olsson Cerebrospinal fluid was analyzed from 8 patients with Creutzfeldt-Jakob disease. No special abnormalities were found concerning cells, total protein content or the concentrations of albumin and IgG. Routine agar gel electrophoresis was normal. Grey and white cerebral matter were...

...P. Bergsholm; H. Skre; S. Mørk A 51-year-old man who died of Creutzfeldt-Jakob disease (CJD), had transient dyskinesias with intention myoclonus and exaggerated startle reaction in early life. This may suggest a link between myoclonic encephalopathy of infants and CJD, and an incubation period...

...Gail Horan; Catherine Keohane; Sophie Molloy; Rachel Howley; Michael Harney; Josephine Heffernan; Christopher McGuigan; Michael Hutchinson; Francesca Brett; Michael Farrell Surveillance for Creutzfeldt-Jakob disease (CJD) has been carried out in the Republic of Ireland since 1980. Initial...