...Yoshiko Watanabe; Shunsuke Mori; Mikiko Ozaki; Shigetoshi Fujiyama; Tatsuo Sato; Masataka Mori Ornithine carbamoyltransferase (OCT), a urea cycle enzyme, is located almost exclusively in liver mitochondria. We designed a sensitive enzyme-linked immunosorbent assay (ELISA) of serum OCT protein using...

...Mikiko Ozaki; Kazutoyo Terada; Masaki Kanazawa; Shigetoshi Fujiyama; Kimio Tomita; Masataka Mori Carbamoylphosphate synthetase I (CPS I), a urea cycle enzyme, is located almost exclusively in the mitochondria of hepatocytes. The enzyme is unique in that it constitutes about 2-6% of total liver...

... or property resulting from any ideas, methods, instructions or products referred to in the content or advertisements. Recombinant DNA Inborn errors Urea cycle Inborn Errors of Metabolism in Humans Enzyme 1991;45:75-80 1607270 Role of Recombinant DNA in Inborn Errors of the Urea Cycle Short Review...

...Denise Christowitz; Frederick J. Mattheyse; John B. Balinsky When 6-week-old rats fed normal diet (22% protein) were transferred to 10 and 7 5 % protein diet, the levels of urea cycle enzymes showed decreases and increases respectively. The activities expressed as units per gram wet weight of liver...

...Linda Brebnor; Elizabeth Phillis; John Balinsky A single injection of glucagon increased the levels of all five urea cycle enzymes in 28-day-old rats, but had no significant effect in 35-day-old animals. Rats weaned onto diets varying in protein content showed rapid adaptation in the levels...

... C. Bachmann Department of Clinical Chemistry, University of Bern, Inselspital, Bern, Switzerland Key Words. Urea cycle Hyperammonemia Essential aminocids Benzoate Arginine Citrulline Serotonin N-carbamoylglutamate Inborn errors of metabolism Abstract. A rapid recognition...

...Q.R. Rogers; J.G. Morris; R.A. Freeland The activities of three urea cycle enzymes, several nitrogen catabolic, gluconeogenic,and lipogenic enzymes were measured in the liver of adult cats fed: a commercial kibble; a 17.5 or 70% protein purified diet, or starved for 5 days. Except for an increase...

... to in the content or advertisements. Urea cycle Citrullinemia Argininosuccinic aciduria Argininosuccinate Argininosuccinate lyase 11 8 2017 1606979 Recent Adv. Inborn Errors of Metabolism. Proc. 4th Int. Congr., Sendai 1987 © 1987 S. Karger AG, Basel Enzyme 38: 227-232 (1987) 0013-9432/87...

...C. Bachmann Hyperammonemia in pediatrics can be due to a number of causes (defects of urea cycle enzymes or transport of its metabolites, organic acidurias, acyl-CoA dehydrogenase or carnitine deficiency, liver bypass or nonspecific insufficiency) requiring differentiated rapid treatment...

...J. P. Colombo In congenital urea cycle disorders, detoxification of ammonia is impaired, leading to hyperammonemia. Ammonia is the major component causing the acute neurological disturbances. It may influence the supply of substrate and its transport at the blood-brain barrier (BBB) which results...

... Aspects of Urea Cycle Enzymes and Related Disorders Masataka Moria, Masaki Takiguchia, Yougo Haraguchia-b, Ichiro Matsudah, Akira Ohiakec, Masaki Takayanagic a Institute for Medical Genetics and b Department of Pediatrics, Kumamoto University Medical School, Kumamoto; c Department of Pediatrics, Chiba...