... Abstract Pulmonary alveolar proteinosis (PAP) is a rare disordercharacterized by abundant deposition of surfactant-like materialin the aveoli. In this article we focus the discussion on theprimary acquired (idiopathic) PAP. We report the studies thatdeveloped the concept that this disorder...

...References References 1. Rosen S, Castleman B, Liebow A: Pulmonary alveolar proteinosis. N Engl J Med 1958;258:1123-1142 2. Trapnell BC, Carey BC, Uchida K, Suzuki T: Pulmonary alveolar proteinosis, a primary immunodeficiency of impaired GM-CSF stimulation of macrophages. Curr Opin...

... Abstract Whole-lung lavage (WLL) is a therapeutic technique for the clearance from alveolar spaces of abnormal material in conditions such as pulmonary alveolar proteinosis. The technique requires the repetitive filling and emptying of the lung with fluid (saline), thus clearing the particulate...

... Society Task Force on CILD in immunocompetent children provided an update on the current understanding of the pathophysiology of these diseases and the ongoing research directions [ 23 ]. In addition, BALF findings usually provide a specific diagnosis in children with alveolar proteinosis, pulmonary...

... 38. McDonald JW, Roggli VL, Bradford WD: Coexisting endogenous and exogenous lipoid pneumonia and pulmonary alveolar proteinosis in a patient with neurodevelopmental disease. Pediatr Pathol 1994;14:505-511 39. Elidemir O, Fan LL, Colasurdo GN: A novel diagnostic method for pulmonary aspiration...

... R, Metze D, Fusenig NE, Breitkreutz D: Vascular anomalities in lipoid proteinosis (hyalinosis cutis et mucosae): basement membrane components and ultrastructure. J Dermatol Sci 2006;42:231-239 ...

... Hemoptysis Pulmonary alveolar proteinosis (rare condition) Contraindications Cardiovascular instability Bleeding diathesis Severe bronchospasm Hypoxemia Complications Bronchospasm Transient fever Infection Pneumothorax Anesthesia Considerations When...

... of patients with lipoid proteinosis also indicate that pericytes contribute to excess deposition of BM [ 49 ]. References References 1. Sims DE: The pericyte - A review. Tissue and Cell 1986;18:153-174 2. Gerhardt H, Betsholtz C: Endothelial-pericyte interactions in angiogenesis. Cell Tissue Res...

..., are often visible signs in this disorder. MonoMAC Syndrome and GATA2 Deficiency A syndrome of monocytopenia with susceptibility to infections with mycobacteria (mainly Mycobacterium avium complex), fungi, HPV and pulmonary alveolar proteinosis has been termed the MonoMAC syndrome. In addition...

..., lymphangio-leiomyomatosis (LAM), chronic idiopathic eosinophilic pneumonia, pulmonary alveolar proteinosis, etc. [ 1 ]. Classification of ILDs. ILDs are separated into four categories: (1) ILDs of known cause, such as those in relation with occupational or environmental exposures, drugs, CTDs...