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epidermolysi

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Book Chapter
Book Chapter
Book Chapter
Series: Current Problems in Dermatology
Volume: 44
Published: 28 May 2013
10.1159/000350009
EISBN: 978-3-318-02404-3
... Abstract Inherited epidermolysis bullosa, which encompasses at least 30 distinctive genetic diseases, may be associated with marked functional impairment, the result of the presence of severe cutaneous and extracutaneous manifestations or complications in some of its subtypes. Inherited...
Book Chapter
Series: Current Directions in Autoimmunity
Volume: 10
Published: 26 May 2008
10.1159/000131455
EISBN: 978-3-8055-8392-3
... Abstract Epidermolysis bullosa acquisita (EBA) is an acquired, mechanobullous disease characterizedby autoimmunity to type VII collagen. Type VII collagen makes anchoring fibrils,structures that connect the epidermis and its underlying basement membrane zone to the papillarydermis. EBA patients...
Book Chapter
Book Chapter
Book Chapter
Series: Current Problems in Dermatology
Volume: 44
Published: 28 May 2013
EISBN: 978-3-318-02404-3
...References References 1. Fine J-D , Hintner H: Life with Epidermolysis Bullosa: Etiology, Diagnosis, and Multidisciplinary Care and Therapy. Wien, Springer, 2009. 2. Fine J-D, Johnson LB, Suchindran C, Moshell A, Gedde-Dahl T: The epidemiology of inherited EB: findings within American...
Book Chapter
Book Chapter
Series: Developments in Ophthalmology
Volume: 45
Published: 11 May 2010
10.1159/000315020
EISBN: 978-3-8055-9419-6
... by chemical and thermal burns (n = 22), pterygium (n = 9), congenital aniridia (n = 6), tumor excision (n = 2), perforating eye injury, mitomycin C, epidermolysis bullosa, bilateral graft-versus-host disease and chlamydial conjunctivitis (each n = 1). Results: Mean follow-up time was 28.5 ± 14.9 months...
Book Chapter
Series: Current Problems in Dermatology
Volume: 11
Published: 02 November 1983
10.1159/000408660
EISBN: 978-3-318-03448-6
... in several diseases, there is no reactivity in the normal, never-blistered skin of patients with dystrophic epidermolysis bull os a (DEB). This suggests that the increased collagenase in the disease may be destroying antigenicity of the antigen recognized by DUX 5.2 or that the antigen may not be present...
Book
Book Chapter
Series: Current Problems in Dermatology
Volume: 50
Published: 01 September 2016
10.1159/000446090
EISBN: 978-3-318-05889-5
... with potent corticosteroids or calcineurin inhibitors [ 63 ]. The benefits include relief of pruritus, pain, and inflammation [ 67 ]. Sequelae such as vulvar stenosis or squamous cell carcinoma are very rare in childhood [ 63 ]. Bullous and Urticarial Dermatoses Epidermolysis bullosa Epidermolysis...
Book
Book Chapter
Series: Monographs in Oral Science
Volume: 30
Published: 08 March 2022
EISBN: 978-3-318-06913-6
... bullous pemphigoid antigen (BPAG2), a hemidesmosomal transmembrane collagen (COL17A1), in generalized atrophic benign epidermolysis bullosa. Nat Genet. 1995 Sep;11(1):83–6. 36. Pulkkinen L, Christiano AM, Gerecke D, Wagman DW, Burgeson RE, Pittelkow MR, et al. A homozygous nonsense mutation...
Book Chapter
Series: Monographs in Oral Science
Volume: 30
Published: 08 March 2022
10.1159/000520764
EISBN: 978-3-318-06913-6
... to the underlying membrane. Mutations in COL17A1 are linked to epithelial recurrent erosion dystrophy and epidermolysis bullosa, junctional, non-Herlitz type [ 35 ]. Mutations in COL17A1 also are linked to 4.4% of cases of amelogenesis imperfecta [ 13 ]. Mutations in LAMB3 or LAMA3 can also lead...
Book Chapter
Series: Current Problems in Dermatology
Volume: 50
Published: 01 September 2016
EISBN: 978-3-318-05889-5
... AT: Prevalence and characterization of pruritus in epidermolysis bullosa. Pediatr Dermatol 2015;32:53-59. 25236506 10.1111/pde.12391 69. Petersen BW, Arbuckle HA, Berman S: Effectiveness of saltwater baths in the treatment of epidermolysis bullosa. Pediatr Dermatol 2015;32:60-63. 25644039 10.1111/pde...
Book
Book Cover Image
Series: Current Problems in Dermatology
Volume: 44
Published: 28 May 2013
10.1159/isbn.978-3-318-02404-3
EISBN: 978-3-318-02404-3
Book Chapter
Series: Current Problems in Dermatology
Volume: 54
Published: 21 August 2018
EISBN: 978-3-318-06385-1
... and ultrastructural changes in dystrophic epidermolysis bullosa resemble skin aging. Aging (Albany NY) 2015;7:389-411. 13. Pang T, Hisamitsu T, Mori H, Shigekawa M, Wakabayashi S: Role of calcineurin B homologous protein in pH regulation by the Na+/H+ exchanger 1: tightly bound Ca2+ ions as important structural...
Book Chapter
Series: Current Problems in Dermatology
Volume: 49
Published: 12 February 2016
10.1159/000441541
EISBN: 978-3-318-05586-3
... and active destruction of the BM. Also, for cells entering the epidermis from the dermis it is likely that active mechanisms allow their passage through the BM [ 67 ]. In general, BM defects result in skin fragility, blistering and recurring wounds, as seen in skin BM disorders such as epidermolysis...
Book Chapter
Series: Aesthetic Dermatology
Volume: 5
Published: 09 February 2021
10.1159/000491842
EISBN: 978-3-318-06690-6
... of the Jessner’s peel allows for keratolysis and epidermolysis. In turn, the TCA is more readily available to the stratum corneum [ 13 ]. Combining TCA 35% and glycolic acid 70% forms the Coleman combination, which allows for medium-depth penetration [ 13 ]. The peel is self-neutralizing and is commonly used...