Objective: To investigate the use of hearing preservation cochlear implantation in children with partial deafness. Patients and Methods: Five children with either drug-induced or congenital partial deafness were enrolled in a pilot study. The patients ranged in age from 13 months to 14 years. Implantation was performed using a hearing preservation technique. A Flex EAS electrode (MED-EL, Innsbruck, Austria) was used in all full insertions. Results: Low frequency hearing was preserved in all patients with postoperative bone conduction within 10 dB of the preoperative hearing levels. These changes were preserved over the follow-up period of 12 months. There were significant improvements in speech perception. Conclusion: Hearing preservation cochlear implantation is a new effective modality in children with partial deafness.

Bodmer D, Brors D, Pak K, Bodmer M, Ryan AF: Gentamicin-induced hair cell death is not dependent on the apoptosis receptor Fas. Laryngoscope 2003;113:452–455.
Clark GM, Black R, Dewhurst DJ, Forster IC, Patrick JF, Tong YC: A multiple-electrode hearing prosthesis for cochlea implantation in deaf patients. Med Prog Technol 1977;5:127–140.
Dorman MF, Gifford RF: Combining acoustic and electric stimulation in the service of speech recognition. Int J Audiol 2010;49:912–919.
Fraysse B, Macías AR, Sterkers O, Burdo S, Ramsden R, Deguine O, Klenzer T, Lenarz T, Rodriguez MM, Von Wallenberg E, James C: Residual hearing conservation and electroacoustic stimulation with the nucleus 24 contour advance cochlear implant. Otol Neurotol 2006;27:624–633.
Gantz BJ, Hansen MR, Turner CW, Oleson JJ, Reiss LA, Parkinson AJ: Hybrid 10 clinical trial: preliminary results. Audiol Neurootol 2009;14(suppl 1):32–38.
Gifford RH, Dorman MF, Brown CA: Psychophysical properties of low-frequency hearing: implications for perceiving speech and music via electric and acoustic stimulation. Adv Otorhinolaryngol 2010;67:51–60.
Gstoettner W, Kiefer J, Baumgartner WD, Pok S, Peters S, Adunka O: Hearing preservation in cochlear implantation for electric acoustic stimulation. Acta Otolaryngol 2004;124:348–352.
Gstoettner WK, van de Heyning P, O’Connor AF, Morera C, Sainz M, Vermeire K, Mcdonald S, Cavallé L, Helbig S, Valdecasas JG, Anderson I, Adunka OF: Electric acoustic stimulation of the auditory system: results of a multi-centre investigation. Acta Otolaryngol 2008;128:968–975.
Gstoettner W, Helbig S, Settevendemie C, Baumann U, Wagenblast J, Arnoldner C: A new electrode for residual hearing preservation in cochlear implantation: first clinical results. Acta Otolaryngol 2009;129:372–379.
Hochmair ES, Hochmair-Desoyer IJ, Burian K: Experience with implanted auditory nerve stimulator. Trans Am Soc Artif Intern Organs 1979;25:357–361.
House WF: The clinical value of single electrode systems in auditory prostheses. Otolaryngol Clin North Am 1978;11:201–208.
Kiefer J, Pok M, Adunka O, Stürzebecher E, Baumgartner W, Schmidt M, Tillein J, Ye Q, Gstoettner W: Combined electric and acoustic stimulation of the auditory system: results of a clinical study. Audiol Neurootol 2005;10:134–144.
Nadol JB Jr, Eddington DK: Treatment of sensorineural hearing loss by cochlear implantation. Annu Rev Med1988;39:491–502.
Niparko JK, Tobey EA, Thal DJ, Eisenberg LS, Wang NY, Quittner AL, Fink NE: Spoken language development in children following cochlear Implantation. JAMA 2010;303:1498–1506.
Prentiss S, Sykes K, Staecker H: Partial deafness cochlear implantation at the University of Kansas: techniques and outcomes. J Am Acad Audiol 2010;21:197–203.
Rajan GP, Kuthubutheen J, Hedne N, Krishnaswamy J: The role of preoperative, intratympanic glucocorticoids for hearing preservation in cochlear implantation: a prospective clinical study. Laryngoscope 2012;122:190–195.
Skarzyński H, Lorens A, D’Haese P, Walkowiak A, Piotrowska A, Sliwa L, Anderson I: Preservation of residual hearing in children and post-lingually deafened adults after cochlear implantation: an initial study. ORL J Otorhinolaryngol Relat Spec 2002;64:247–253.
Skarzynski H, Lorens A, Piotrowska A, Anderson I: Partial deafness cochlear implantation provides benefit to a new population of individuals with hearing loss. Acta Otolaryngol 2006;126:934–940.
Skarzynski H, Lorens A, Piotrowska A, Anderson I: Partial deafness cochlear implantation in children. Int J Pediatr Otorhinolaryngol 2007;71:1407–1413.
Skarzynski H, Lorens A, Piotrowska A, Anderson I: Preservation of low frequency hearing in partial deafness cochlear implantation (PDCI) using the round window surgical approach. Acta Otolaryngol 2007;127:41–48.
Turner CW, Gantz BJ, Karsten S, Fowler J, Reiss LA: Impact of hair cell preservation in cochlear implantation: combined electric and acoustic hearing. Otol Neurotol 2010;31:1227–1232.
Usami S, Moteki H, Suzuki N, Fukuoka H, Miyagawa M, Nishio SY, Takumi Y, Iwasaki S, Jolly C: Achievement of hearing preservation in the presence of an electrode covering the residual hearing region. Acta Otolaryngol 2011;131:405–412.
von Ilberg C, Kiefer J, Tillein J, Pfenningdorff T, Hartmann R, Stürzebecher E, Klinke R: Electric-acoustic stimulation of the auditory system. New technology for severe hearing loss. ORL J Otorhinolaryngol Relat Spec 1999;61:334–340.
Wilson BS, Lawson DT, Finley CC, Wolford RD: Coding strategies for multichannel cochlear prostheses. Am J Otol1991;12(suppl):56–61.
Zhang T, Dorman MF, Spahr AJ: Information from the voice fundamental frequency (F0) region accounts for the majority of the benefit when acoustic stimulation is added to electric stimulation. Ear Hear 2010;31:63–69.
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